S�NDROME DE RETT: abordagem odontol�gica

Clarissa Barroso Chirano; Gimol Benchimol Resende; Eliane Aranha de Oliveira Ribeiro; Keuly Souza Soares

S�NDROME DE RETT: abordagem odontol�gica

Clarissa Barroso Chirano, Gimol Benchimol Resende, Eliane Aranha de Oliveira Ribeiro, Keuly Souza Soares

Resumo

A S�ndrome de Rett (SR) � uma desordem de desenvolvimento neurol�gico que afeta primariamente mulheres, caracterizada por severa defici�ncia f�sica e cognitiva que se manifesta geralmente a partir dos 6 meses de vida. Clinicamente � identificada por comportamento autista, perda de express�o facial e movimento estereotipado das m�os. Tem sua origem relacionada a muta��o no cromossomo X, especificamente no gene MECP2. Este trabalho tem por objetivo apresentar, atrav�s de um relato de caso, os aspectos gerais do manejo no atendimento odontol�gico realizado em paciente diagnosticado com SR. Concluiu-se que, � poss�vel fornecer o atendimento ambulatorial odontol�gico a estes pacientes, promovendo assim sa�de bucal, prevenindo agravos a sa�de geral e contribuindo com a qualidade de vida dos mesmos.

Palavras-chave

S�ndrome de Rett, Doen�as raras, Sa�de bucal

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