Histiocitose de Células de Langerhans
Resumo
A histiocitose de células de Langerhans é uma doença rara proliferativa de etiologia desconhecida que pode ocorrer a qualquer idade, mas é predominante em crianças. Tem apresentação e evolução clinica variável, podem ocorrer lesões localizadas ou disseminadas que podem regredir espontaneamente ou comprometer órgãos vitais com consequências graves. O presente artigo, descreve o caso de uma criança do gênero masculino com um ano e sete meses de idade, apresentando aumento de volume na face. Relatam-se o manejo e a evolução, destacando a importância do diagnóstico precoce e diferencial.
Palavras-chave: Histiocitose de células de Langerhans; Transtornos histiocíticos malignos, Odontologia.
Abstract
Langerhans cell histiocytosis is a rare proliferative disease of unknown etiology that can occur at any age, but is prevalent in children. Has presentation and variable clinical course, there may be localized or disseminated lesions that may regress spontaneously or compromise vital organs with serious consequences. This article describes the case of a male child with one year and seven months, an increase of volume in the face. Report to the management and development, highlighting the importance of early diagnosis and differential.
Keywords: Histiocytosis, Langerhans-Cell; Histiocytic Disorders, Malignant; Dentistry.
Texto completo:
PDFRefer?ncias
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Apontamentos
- N?o h? apontamentos.
Direitos autorais 2015 Revista Virtual da AcBO - ISSN 2316-7262
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